A newly-defined entity: combined pulmonary fibrosis and emphysema syndrome

Ozcelik N., Ozsu S.

TUBERKULOZ VE TORAK-TUBERCULOSIS AND THORAX, vol.63, no.1, pp.48-52, 2015 (ESCI) identifier identifier identifier

  • Publication Type: Article / Review
  • Volume: 63 Issue: 1
  • Publication Date: 2015
  • Doi Number: 10.5578/tt.7747
  • Journal Name: TUBERKULOZ VE TORAK-TUBERCULOSIS AND THORAX
  • Journal Indexes: Emerging Sources Citation Index (ESCI), Scopus, TR DİZİN (ULAKBİM)
  • Page Numbers: pp.48-52
  • Recep Tayyip Erdoğan University Affiliated: No

Abstract

Combined pulmonary fibrosis and emphysema (CPFE) syndrome is a rare disease characterized with shortness of breath, upper lobe emphysema, lower lobe fibrosis and impairment of gas exchange. This syndrome is a disease usually seen in male smokers. Pulmonary hypertension is associated with mortality. Another important feature, spirometric volumes relatively protected and a reduction in carbon monoxide diffusion test. CPFE syndrome in the literature so far have been identified in only 70 patients. In this review CPFE syndrome is presented with literature.